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Nutritional and metabolic disorders
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Nutritional and metabolic disorders
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(48)
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(1)
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(2)
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(1)
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(6)
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(32)
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(11)
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Velaglucerase alfa
Caplacizumab
What advice should be given to patients with porphyria who intend to travel?
20 December 2019
·
Most travel vaccines are safe in the acute porphyrias, but there has been an unpublished report of an acute porphyria attack following yellow fever vaccination.…
Alglucosidase alfa
Aluminium hydroxide
Safety in Lactation: Fluids and electrolytes
23 September 2020
·
Oral and intravenous products for correcting fluid and electrolyte imbalance will present no risk to a breastfeeding infant as they are normally present in milk.…
Safety in Lactation: Minerals
5 November 2020
·
Maternal mineral supplements pose no risk to breastfed infants when taken in normal doses, although their use should be unnecessary unless the mother’s nutritional status…
Using haem arginate (human hemin) in acute porphyria attacks
21 June 2022
·
Understanding when and how to use haem arginate can help individuals at risk of acute neurovisceral attacks, which though uncommon may be life threatening.
Trientine
Nitisinone
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